2. Academic Validation
  3. Klippel-Trenaunay-Weber Syndrome with Kasabach-Merritt Coagulopathy and Hydronephrosis

Klippel-Trenaunay-Weber Syndrome with Kasabach-Merritt Coagulopathy and Hydronephrosis

  • Indian Pediatr. 2015 Nov;52(11):987-8. doi: 10.1007/s13312-015-0760-5.
Lata Bhat 1,  Supriya Bisht,  Kavita Khanijo
Affiliations

Affiliation

  • 1 Department of Neonatology, Fortis Hospital, Noida, Uttar Pradesh, India. Correspondence to: Dr Supriya Bisht, Department of Neonatology, Fortis Hospital, B-22, Sector 62, Noida, Uttar Pradesh, India. supriyabisht07@gmail.com.
PMID: 26615353 DOI: 10.1007/s13312-015-0760-5
Abstract

Background: Klippel-Trenaunay-Weber Syndrome is a rare syndrome, consisting of vascular malformation of blood and lymph vessels.

Case characteristics: A newborn female with respiratory distress from birth, and having vascular malformation involving left thigh.

Observation: The neonate also had hydronephrosis and developed complication of Kasabach Merritt syndrome.

Message: Urogenital abnormalities can be present in Klippel-Trenaunay-Weber syndrome but hydronephrosis is rare. Mortality is high with development of Kasabach Merritt syndrome.

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