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Results for "

leukodystrophy

" in MedChemExpress (MCE) Product Catalog:

5

Inhibitors & Agonists

1

Biochemical Assay Reagents

1

Natural
Products

Cat. No. Product Name Target Research Areas Chemical Structure
  • HY-136490
    Psychosine

    Galactosylsphingosine

    		 PKC Neurological Disease Cancer
    Psychosine (Galactosylsphingosine), a substrate of the galactocerebrosidase (GALC) enzyme, is a potential biomarker for Krabbe disease . Psychosine is a highly cytotoxic lipid, capable of inducing cell death in a wide variety of cell types including, most relevantly to globoid cell leukodystrophy (GLD), oligodendrocytes. Psychosine causes cell death at least in part via apoptosis. Psychosine also is an inhibitor of PKC .
    Psychosine
  • HY-145535
    Tetracosanoyl-sulfatide

    C24 3'-sulfo Galactosylceramide (d18:1/24:0)

    		 Endogenous Metabolite Metabolic Disease
    Tetracosanoyl-sulfatide is an endogenous metabolite present in Urine that can be used for the research of Mild Metachromatic Leukodystrophy .
    Tetracosanoyl-sulfatide
  • HY-B1680
    Lithium citrate

    Litarex

    		 Others Neurological Disease
    Lithium citrate is a lithium supplement that reduces excess brain N-acetylaspartate (NAA) in Canavan disease. Canavan disease is an autosomal recessive leukodystrophy caused by mutations in the aspartate acylase (ASPA) gene, which catalyzes the hydrolysis of N-acetylaspartate (NAA) to acetate and aspartate .
    Lithium citrate
  • HY-158725
    N-Octadecenoyl-(cis-9)-sulfatide

    		Endogenous Metabolite Others
    N-Octadecenoyl-(cis-9) -Sulfatide is a glycolipid found in the brains of mice. N-Octadecenoyl-(cis-9) -Sulfatide can be used as a standard for the determination of C18:13 '-mergogalactosyllactose in dry blood stains of patients with chromatic leukodystrophy (MLD) by ultra-high performance liquid chromatography-mass spectrometry (UPLC-MS) .
    N-Octadecenoyl-(cis-9)-sulfatide
  • HY-E70181
    Galactosylceramidase

    EC:3.2.1.46; GALC

    		 Ceramidase Others
    Galactosylceramidase involves in lysosomal catabollsm of galactosytceramide. Galactosylceramidase can be used in study Krabbe disease .
    Galactosylceramidase

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